
ANGIOMIOLIPOMA EPITELIOIDE RENAL
Igor Azurmendi Arin, Roberto Llarena Ibarguren, Jorge García-Olaverri Rodríguez, Ivan Olano Grasa, Emilio Cantón Aller, Carlos Pertusa Peña
ANGIOMIOLIPOMA EPITELIOIDE RENAL
OBJECTIVE: To issue the existence of a va-riety of angiomyolipoma, named epithelioid, with differenthistological and clinic properties.METHODS: We report the case of a 17-year-old female,with Bourneville’s disease, who was discovered to have asolid renal mass suggestive of carcinoma in a control CTscan, adjacent to other smaller masses identified as angio-myolipomas.RESULTS: After several tumorectomies, the suspicious mass,4 cm in size, was diagnosed as epithelioid angiomyolipo-ma, with immunohistochemical confirmation of capacity forHMB45, and negative vimentin and keratin.CONCLUSIONS: Despite the possibility of coexistence ofadenocarcinoma and angiomyolipoma, the existence of anepithelioid variety cannot be discarded, mainly in patientswith phakomatosis. The indications for surgery are the samethan for the rest of renal masses. Nevertheless, follow-upcriteria must be stricter due to the possibility of torpid out-come in terms of dissemination of this infrequent variety ofangiomyolipoma
Angiomyolipoma / Epithelioid / Phakoma-tosis {{custom_keyword}} /
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