OBJECTIVE: To report two additional cases ofSchönlein-Henoch purpura that developed acute scrotum.METHODS: Two patients with Schönlein-Henoch purpura thatdeveloped acute scrotum in the course of the disease are presented.The literature is briefly reviewed and discussed.RESULTS / CONCLUSIONS: Schönlein-Henoch purpura is asystemic vasculitis with involvement of the genital area in 15% of thecases and must be distinguished from testicular torsion. The clinicalfeatures, the findings at physical examination and scrotal ultrasoundevaluation should suffice to make the correct diagnosis and avoidsurgery. However, if the findings are inconclusive, techniques usingisotopes and/or echo-Doppler can be utilized. If these are notavailable, exploratory scrototomy should not be delayed. Excellentresponse is achieved with steroid therapy.